購物車
幫助
021-54845833/15800441009
中文名稱： EHHADH抗原（重組蛋白）
英文名稱： EHHADH Antigen (Recombinant Protein)
別 名： LBP; ECHD; LBFP; PBFE; L-PBE
儲 存： 冷凍（-20℃）
相關(guān)類別： 抗原
概 述：
|
Fusion protein corresponding to a region derived from 283-572 amino acids of human EHHADH |
|
Full name: |
enoyl-CoA, hydratase/3-hydroxyacyl CoA dehydrogenase |
|
Synonyms: |
LBP; ECHD; LBFP; PBFE; L-PBE |
|
Swissprot: |
Q08426 |
|
Gene Accession: |
BC038948 |
|
Purity: |
>85%, as determined by Coomassie blue stained SDS-PAGE |
|
Expression system: |
Escherichia coli |
|
Tags: |
His tag C-Terminus, GST tag N-Terminus |
|
Background: |
The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene. |
